Diagnostic Predicament of Persistent Electrolyte Imbalance in a Neonate, Pseudohypoaldosteronism (PHA)

Pseudohypoaldosteronism (PHA) type 1 is a heterogeneous group of disorder electrolyte metabolism characterized by apparent renal tubular unresponsiveness to aldosterone action. PHA-1 manifested hyponatremia, hyperkalemia, metabolic acidosis and may present as salt wasting crisis with elevated levels renin aldosterone. subdivided into two types varying degree severity. The earliest sign both poor weight gain due dehydration failure thrive during infancy. Here, we report case in 30 days old female infant who presented mild hyperkalemia was treated dietary sodium chloride supplementation, potassium binding resin fluid replacement therapy which proved be lifesaving.